Stenting of the right ventricular outflow tract with subsequent radical correction in a child with a tetralogy of Fallot: results of six-year follow-up
https://doi.org/10.23946/2500-0764-2020-5-3-98-105
Abstract
Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart defect. Since the first radical correction in 1954, treatment strategy has been constantly improving. Current treatment of ToF ensures the long-term survival (30-year survival ranges from 68.5% to 90.5%), yet it is still challenging in underweight patients. Here we present a clinical case of two-step surgery which included right ventricular outflow tract (RVOT) stenting and further radical correction in an underweight child who was then followed-up for six years. RVOT stenting is an appropriate alternative to the bypass surgery which has higher risk of perioperative complications. RVOT stenting significantly reduces hypoxia, enhances the development of the pulmonary vasculature and increases end-diastolic index ultimately permitting efficient radical correction after 4 months. The described approach resulted in a favorable outcome and quality of life after 6 years of follow-up.
Keywords
congenital heart disease,
tetralogy of Fallot,
right ventricular outflow tract stenting,
long-term outcomes
Supporting agencies: This research was funded by the Complex Program of Basic Research under the Siberian Branch of the Russian Academy of Sciences within the Basic Research Topic of Research Institute for Complex Issues of Cardiovascular Diseases № 0546- 2019-0003 “Atherosclerosis and its comorbidities. Features of diagnostics and risk management in a large industrial region of Siberia”.
About the Authors
A. A. Lyapin
Research Institute for Complex Issues of Cardiovascular Diseases
Russian Federation
Russian Federation
Dr. Anton A. Lyapin, MD, PhD Student
6, Sosnovy Boulevard, Kemerovo, 650002
I. K. Khalivopulo
Research Institute for Complex Issues of Cardiovascular Diseases
Russian Federation
Russian Federation
Dr. Ivan K. Khalivopulo, MD, Head of the Cardiovascular Surgery Unit
6, Sosnovy Boulevard, Kemerovo, 650002
P. A. Shushpannikov
Research Institute for Complex Issues of Cardiovascular Diseases
Russian Federation
Russian Federation
Dr. Pavel A. Shushpannikov, MD, Cardiovascular Surgeon, Cardiovascular Surgery Unit
6, Sosnovy Boulevard, Kemerovo, 650002
R. S. Tarasov
Research Institute for Complex Issues of Cardiovascular Diseases
Russian Federation
Russian Federation
Dr. Roman S. Tarasov, MD, DSc, Head of the Laboratory for Endovascular and Reconstructive Cardiovascular Surgery, Department of Cardiovascular Surgery
6, Sosnovy Boulevard, Kemerovo, 650002
References
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Review
For citations:
Lyapin A.A., Khalivopulo I.K., Shushpannikov P.A., Tarasov R.S. Stenting of the right ventricular outflow tract with subsequent radical correction in a child with a tetralogy of Fallot: results of six-year follow-up. Fundamental and Clinical Medicine. 2020;5(3):98-105. (In Russ.) https://doi.org/10.23946/2500-0764-2020-5-3-98-105
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